Image of Red blood cells to illustrate the link between Hermansky-Pudlak Syndrome, HPS, and its bleeding disorder.The bleeding disorder of HPS is considered to be ‘mild’ in comparison to other more serious bleeding disorders such as Haemophila.  In day to day living this bleeding disorder can be inconvenient and sometimes distressing, but it is quite possible to live a normal active life.

The pattern and severity of bleeding symptoms associated with HPS vary between people. For instance,  one person might experience regular nosebleeds but may rarely see blood when they brush their teeth, the opposite may be true for another person. Similarly, one person might bruise easily but not have nosebleeds.  Many women experience heavy periods but some do not, etc.

Typical symptoms can include

However, there are circumstances in which the bleeding disorder of HPS can be more serious and when it is necessary to take precautions or steps to reduce bleeding and improve blood clotting.  Bleeding is typically more serious when a person does not know they have HPS.  When a person has been diagnosed with HPS it is possible for them and their doctors to  take steps to minimise the risk of prolonged or excessive bleeding.

The following are circumstances that may require special steps to reduce prolonged bleeding or steps to improve blood clotting.

(Read more about the bleeding disorder of HPS, Obstetrics, and Gynecology)

(Read more about the ‘Crohn’s like’ colitis associated with HPS)

General points about controlling bleeding in HPS

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The bleeding disorder of Hermansky-Pudlak Syndrome